The paper presents the case of a 48-year-old patient who had been experiencing tinnitus and pulsations in the right ear for two years. The patient was consulted on an outpatient basis by an otolaryngologist, who found no abnormalities on physical examination. Upon admission to the neurology department, the patient had no abnormalities on neurological examination. During hospitalisation, classic digital subtraction angiography of the cerebral arteries revealed a vascular malformation in the form of a meningeal arteriovenous fistula located at the base of the skull, in the opening of the right internal jugular vein. The patient was treated with endovascular embolisation with a good clinical outcome. Recognising and treating a vascular malformation can prevent complications such as intracranial haemorrhage, as well as improve quality of life by reducing the severity of symptoms.